Cutaneous lung tissue heterotopia is a very rare disorder where mature lung tissues develop in the skin. This is only the second known report of cutaneous lung tissue heterotopia, with the first by Singer et al. in 1998. A newborn infant had a hemangioma-like, freely movable mass connected to the anterior aspect of the sternal manubrium. Pathologic findings showed mature lung tissues with bronchi, bronchioles, and alveoli through the dermis and subcutis, and it was diagnosed as cutaneous lung tissue heterotopia. Cutaneous lung tissue heterotopia is hypervascular, so grossly it looks like a hemangioma. It can be differentiated from pulmonary sequestration, teratoma, bronchogenic cyst, and branchial cleft cyst by histology and the location of the mass. We describe the clinical, radiologic, and pathologic findings of a cutaneous lung tissue heterotopia, the first reported in Korea...reference :http://jkms.org/search.php?where=av...387&code=0063JKMS&vmode=PUBREADER#!po=8.33333 J Korean Med Sci. 2010 Sep;25(9):1387-1389. English. Published online 2010 August 12. http://dx.doi.org/10.3346/jkms.2010.25.9.1387 © 2010 The Korean Academy of Medical Sciences. The First Korean Case of Cutaneous Lung Tissue Heterotopia Ga Won Jeon,1 Seong Woo Han,1 Ji Mi Jung,1 Mi Seon Kang,2 and Jong Beom Sin[Broken External Image]:http://synapse.koreamed.org/image/icon_corresp.gif1 1Department of Pediatrics, Inje University College of Medicine, Busan Paik Hospital, Busan, Korea. 2Department of Pathology, Inje University College of Medicine, Busan Paik Hospital, Busan, Korea. [Broken External Image]:http://synapse.koreamed.org/image/icon_corresp.gif Address for Correspondence: Jong Beom Sin, M.D. Department of Pediatrics, Busan Paik Hospital, Inje University College of Medicine, 75 Bokji-ro, Busanjin-gu, Busan 614-735, Korea. Tel: +82.51-890-6126, Fax: +82.51-895-7785, Email: [email protected] Received September 02, 2009; Accepted November 30, 2009. This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited. Go to:Abstract Cutaneous lung tissue heterotopia is a very rare disorder where mature lung tissues develop in the skin. This is only the second known report of cutaneous lung tissue heterotopia, with the first by Singer et al. in 1998. A newborn infant had a hemangioma-like, freely movable mass connected to the anterior aspect of the sternal manubrium. Pathologic findings showed mature lung tissues with bronchi, bronchioles, and alveoli through the dermis and subcutis, and it was diagnosed as cutaneous lung tissue heterotopia. Cutaneous lung tissue heterotopia is hypervascular, so grossly it looks like a hemangioma. It can be differentiated from pulmonary sequestration, teratoma, bronchogenic cyst, and branchial cleft cyst by histology and the location of the mass. We describe the clinical, radiologic, and pathologic findings of a cutaneous lung tissue heterotopia, the first reported in Korea.