Microtia, is a congenital deformity affecting the outer ear (pinna) where the ear does not fully develop during the first trimester of pregnancy. A Microtia ear is often smaller in size, can have a peanut shaped appearance, only have a small nub or lobe present, or be completely absent at birth. Microtia is Latin for the words micro and otia, meaning “little ear.” Microtia can affect one ear (unilaterally) or both ears (bilaterally). Microtia occurs in every 1 out of 6,000 to 12,000 births. The right ear is more commonly affected. Microtia is often accompanied by Atresia.
Goldenhar Syndrome should also be suspected... Goldenhar syndrome is a rare congenital condition characterized by abnormal development of the eye, ear and spine.